by Michael Nace | Dec 20, 2018 | Nursing Resource Page Three, Nursing Resource Pages, Nutritionist Resource Page One, Nutritionist Resource Pages, Pediatricians Resource Page One, Pediatricians Resources
Feeding is often a challenge in people with spinal muscular atrophy (SMA), particularly in those with more severe forms, and feeding difficulties can lead to malnutrition and suboptimal body composition.1,2 Loss of ability to sit is associated with the need for...
by Michael Nace | Nov 28, 2018 | Neurologists Resource Page Three, Neurologists Resource Pages, Nursing Resource Page Three, Nursing Resource Pages, Pediatricians Resource Page Two, Pediatricians Resources, Radiology Resource Page Three, Radiology Resources
In the pivotal clinical trials that support FDA approval, nusinersen was administered via intrathecal injection. However, this approach requires that patients receive multiple intrathecal injections separated in time by weeks. During each infusion, the clinician must...
by Michael Nace | Oct 30, 2018 | Nursing Resource Page Three, Nursing Resource Pages, Orthopedics Resource Page Three, Orthopedics Resource Pages, Pediatricians Resource Page Three, Pediatricians Resources, Physical Therapists Resource Page Three, Physical Therapists Resource Pages
Poor bone health is a consequence of Spinal Muscular Atrophy (SMA). Bone mineral density is significantly reduced1,2 in up to 50% of patients with SMA.3 Immobility and muscle weakness in SMA are significant risk factors for low bone mineralization, but bone density is...
by Michael Nace | Oct 15, 2018 | Nursing Resource Page Three, Nursing Resource Pages, Nutritionist Resource Page Two, Nutritionist Resource Pages
Patients with Spinal Muscular Atrophy (SMA) have nutritional needs that vary depending on their ages, the severity of their weakness (non-sitter versus sitter), and the acuity of their situation.1 Chronic Hydration Needs SMA is associated with dysphagia and gastric...
by Michael Nace | Sep 4, 2018 | Nursing Resource Page Three, Nursing Resource Pages, Nutritionist Resource Page Three, Nutritionist Resource Pages
Spinal Muscular Atrophy (SMA) is a progressive, degenerative neuromuscular disease. Patients with several forms of SMA, specifically, types 0, 1, and severe type 2, do not have a normal life expectancy and will have deaths attributable to the sequelae of SMA.1-3 In...
by Michael Nace | Aug 15, 2018 | Just Published, Nursing Resource Page Three, Nursing Resource Pages, Orthopedics Resource Page One, Orthopedics Resource Pages, Pediatricians Resources
Children with spinal muscular atrophy (SMA) face several orthopedic challenges including scoliosis, joint flexion contractures, subluxations and dislocations of the hip, and bone fractures.1,2 By far the most common orthopedic problem in SMA patients is a progressive,...
