Assistive Devices and Equipment in Spinal Muscular Atrophy: Feeding

Assistive Devices and Equipment in Spinal Muscular Atrophy: Feeding

by | Dec 20, 2018 | Nursing Resource Page Three, Nursing Resource Pages, Nutritionist Resource Page One, Nutritionist Resource Pages, Pediatricians Resource Page One, Pediatricians Resources

Feeding is often a challenge in people with spinal muscular atrophy (SMA), particularly in those with more severe forms, and feeding difficulties can lead to malnutrition and suboptimal body composition.1,2 Loss of ability to sit is associated with the need for...
Alternate Nusinersen Administration Strategies

Alternate Nusinersen Administration Strategies

by | Nov 28, 2018 | Neurologists Resource Page Three, Neurologists Resource Pages, Nursing Resource Page Three, Nursing Resource Pages, Pediatricians Resource Page Two, Pediatricians Resources, Radiology Resource Page Three, Radiology Resources

In the pivotal clinical trials that support FDA approval, nusinersen was administered via intrathecal injection. However, this approach requires that patients receive multiple intrathecal injections separated in time by weeks. During each infusion, the clinician must...
Spinal Muscular Atrophy: Fractures

Spinal Muscular Atrophy: Fractures

by | Oct 30, 2018 | Nursing Resource Page Three, Nursing Resource Pages, Orthopedics Resource Page Three, Orthopedics Resource Pages, Pediatricians Resource Page Three, Pediatricians Resources, Physical Therapists Resource Page Three, Physical Therapists Resource Pages

Poor bone health is a consequence of Spinal Muscular Atrophy (SMA). Bone mineral density is significantly reduced1,2 in up to 50% of patients with SMA.3 Immobility and muscle weakness in SMA are significant risk factors for low bone mineralization, but bone density is...